Rare and Interstitial Lung Diseases,1/e > Respiratory Medicine

Written and edited by global leaders in this challenging field, Rare and Interstitial Lung Diseases: Clinical Cases and Real-World Discussions brings you up to date with the latest advances in complex or rare lung diseases managed on outpatient or inpatient respiratory or critical care units. Using a unique, case-based approach, a wide variety of cases are presented along with perspectives from a multidisciplinary team of experts who discuss therapeutic choices and rationales. This real-world approach allows the reader to become a virtual attending physician, simulating a realistic clinical reasoning process on the diagnosis, treatment, and follow-up of patients with rare and complex lung diseases.
Reflects a nuanced, multidisciplinary, evidence-based approach to diagnoses, treatment options, and follow-up criteria for complex and rare pulmonary disorders such as idiopathic pulmonary fibrosis, interstitial lung disease related to connective tissue diseases, hypersensitivity pneumonitis, sarcoidosis, and pulmonary vascular disease.
Each case includes onset of symptoms, diagnostic/therapeutic path, and discussions on the clinical choices made in accordance with evidence-based medical procedures.
Describes each clinical and laboratory finding and features 150 images, including plain film, procedural photos, ultrasound images, CT scans, and histopathology specimens.
Includes the most recent updates to international guidelines (ATS/ERS/JRS/ALAT) on idiopathic pulmonary fibrosis (IPF).
Covers the progression of pulmonary fibrosis in patients with ILD other than IPF; the role of transbronchial lung cryobiopsy (TBLC) in obtaining a tissue diagnosis in patients with undiagnosed ILD; and the indications of antifibrosant drugs.
A practical and interactive resource for pulmonologists, as well as critical care and internal medicine practitioners and fellows, thoracic surgeons, and thoracic radiologists.
Enhanced eBook version included with purchase. Your enhanced eBook allows you to access all of the text, figures, and references from the book on a variety of devices. Additional digital ancillary content may publish up to 6 weeks following the publication date. 

PART I Fibrosing Interstitial Lung Diseases

1 Fibrotic Hypersensitivity Pneumonitis After Long-Term Exposure to Household Mold
2 Idiopathic Pulmonary Fibrosis with a Typical Usual Interstitial Pneumonia Pattern on Chest High-Resolution Computed Tomography
3 Idiopathic Pulmonary Fibrosis in a Smoker with Indeterminate Usual Interstitial Pneumonia Pattern on High-Resolution Computed Tomography
4 Interstitial Lung Abnormalities Evolving to Histologically Proven Nonspecific Interstitial Pneumonia

PART II Smoking-Associated Interstitial Lung Diseases

5 Respiratory Bronchiolitis-Interstitial Lung Disease
6 Desquamative Interstitial Pneumonia Complicated by Glucocorticoid-Induced Osteonecrosis of the Femoral Head in a Former Smoker
7 Pulmonary Langerhans Cell Histiocytosis in a Young Man Complaining of a Dry Cough and Exertional Dyspnea
8 Combined Pulmonary Fibrosis and Emphysema in a Smoker with Apparently Normal Lung Volumes
PART III Granulomatous Lung Diseases
9 Swollen Cervical Lymph Nodes and Centrilobular Pulmonary Nodules Due to Sarcoidosis
10 Relapsing Pulmonary Infiltrates, Severe Asthma, and Eosinophilia with Systemic Manifestations
11 Diffuse Parenchymal Lung Disease with Granulomas in the Colon and Cervical Lymph Nodes Due to Tuberculosis

PART IV Connective Tissue Disease–Associated Lung Diseases

12 Pulmonary Fibrosis and Solitary Pulmonary Nodule in Hidden Rheumatoid Arthritis
13 Interstitial Lung Disease with High-Resolution Computed Tomography Pattern of Usual Interstitial Pneumonia in a Patient with Unknown Systemic Sclerosis
14 Interstitial Lung Disease Associated with the Antisynthetase Syndrome

PART V Rare and Ultra-Rare Interstitial Lung Diseases

15 Pulmonary Alveolar Microlithiasis: An Ultra-Rare Disease
16 Pulmonary Alveolar Proteinosis in a Woman with Respiratory Failure and Crazy-Paving Pattern on Chest Computed Tomography
17 Idiopathic Pleuroparenchymal Fibroelastosis in a Never-Smoker Woman with a History of Hypersensitivity Pneumonitis
18 IgG4-Related Disease as an Unexpected Cause of Hemoptysis

PART VI Miscellanea

19 Amyloid-Associated Cystic Lung Disease in a Woman with Sjögren Syndrome
20 Sporadic Lymphangioleiomyomatosis in a Woman Previously Diagnosed with Asthma
21 Acute Respiratory Failure in a Patient with Diffuse Ground-Glass Opacities During the COVID-19 Pandemic
Index